1. Formation of a traumatic air cyst and ensuing hemopneumothorax during CT angiography in a patient with Ehlers-Danlos syndrome
- Author
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Christopher S. Morris, Joseph T Shields, Anant D Bhave, Geoffrey M Scriver, William Parkinson, Hans Michell, Prajna Chopra, and Naiim Ali
- Subjects
0303 health sciences ,medicine.medical_specialty ,medicine.diagnostic_test ,business.industry ,Connective tissue ,Case Report ,General Medicine ,medicine.disease ,Surgery ,03 medical and health sciences ,0302 clinical medicine ,medicine.anatomical_structure ,Ehlers–Danlos syndrome ,030220 oncology & carcinogenesis ,Angiography ,medicine ,Cyst ,business ,Hemopneumothorax ,030304 developmental biology - Abstract
Ehlers-Danlos syndrome (EDS) refers to a rare group of genetic disorders that makeup part of the connective tissue disorders consortium. It is characterized by clinical features such as skin hyperextensibility, joint hypermobility, and tissue fragility. A vascular subtype (EDS IV) exists, that predisposes affected patients to vascular injury and is well-known and documented. However, other manifestations of EDS IV are less commonly understood and reported. Though spontaneous pneumothorax has been described in several cases, formation of traumatic air cysts/pneumatoceles with little to no inciting factors has not. This can eventually lead to pulmonary hemorrhage or hemopneumothorax. We present a case of spontaneous formation of a traumatic air cyst with ensuing large-volume hemopneumothorax occurring in a time period of under 3 minutes, between pre- and post-contrast-media administration during CT angiography of the chest.
- Published
- 2020