1. Takotsubo syndrome and left ventricular non-compaction cardiomyopathy: Casualty or causality?
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Del Buono, Marco Giuseppe, Montone, Rocco Antonio, Camilli, Massimiliano, Gurgoglione, Filippo Luca, Ingrasciotta, Gessica, Meucci, Maria Chiara, Fracassi, Francesco, Niccoli, Giampaolo, and Crea, Filippo
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CARDIOMYOPATHIES , *SYNDROMES - Abstract
Abstract Takotsubo syndrome (TS) is a condition of transient regional ventricular systolic dysfunction, usually presenting with acute chest pain and/or dyspnea, that is increasingly recognized especially in post-menopausal women following a psychological or physical stress. Initially considered as a benign condition with an isolated and self-limiting episode, it is now recognized that it is associated with a significant risk of in-hospital mortality and of recurrence. We herein describe a case of a 61-year-old female with left ventricular non-compaction cardiomyopathy (LVNC) who experienced a recurrence of TS, highlighting the potential pathophysiological role for LVNC in predisposing this syndrome and its recurrence. Moreover, we underscored possible therapeutic implications deriving from this case. Highlights • Takotsubo syndrome (TS) is an acute form of neurocardiogenic stunning. • Altered autonomic-limbic processing supports brain-heart axis in TS. • Sympathetic activation with catecholamine release, causes myocardial toxicity and/or coronary microvascular dysfunction. • Left ventricular non-compaction cardiomyopathy (LVNC) is a rare disease characterized by a subverted myocardial architecture. • LVNC may predispose to TS because associated with coronary microvascular and autonomic dysfunction. [ABSTRACT FROM AUTHOR]
- Published
- 2019
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