1. Anesthetic Management for an Adult With Glycogen Storage Disease Type 0.
- Author
-
Sakamizu A, Yaguchi E, and Hamaguchi S
- Subjects
- Adult, Anesthesia, General adverse effects, Anesthesia, Intravenous, Anesthetics, Intravenous, Female, Humans, Remifentanil, Young Adult, Glycogen Storage Disease, Propofol
- Abstract
A 20-year-old woman with glycogen storage disease type 0 (GSD-0) underwent velopharyngeal closure for velopharyngeal insufficiency following palatoplasty. To reduce the risk of complications attributed to GSD-0, general anesthesia was administered using a total intravenous anesthesia (TIVA) technique with propofol and remifentanil, along with supplemental glucose-containing intravenous fluids. Her blood glucose remained stable, intraoperative body temperature ranged from 36.5 to 37.2°C, and the velopharyngeal closure was completed without any adverse events., (© 2020 by the American Dental Society of Anesthesiology.)
- Published
- 2020
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