1. Persistent müllerian duct syndrome with torsion of an intra-abdominal seminoma
- Author
-
Michiels G and Masereel B
- Subjects
Adult ,Male ,medicine.medical_specialty ,Pathology ,Torsion Abnormality ,Mullerian Ducts ,medicine.medical_treatment ,Uterus ,Disorders of Sex Development ,Testicular Neoplasms ,Internal medicine ,Laparotomy ,medicine ,Humans ,Abdomen, Acute ,business.industry ,General Medicine ,Seminoma ,Syndrome ,medicine.disease ,Endocrinology ,medicine.anatomical_structure ,Acute abdomen ,Male pseudohermaphroditism ,Persistent Müllerian duct syndrome ,Vagina ,Surgery ,medicine.symptom ,business - Abstract
Persistent Mullerian Duct Syndrome (PMDS) is a particular form of male pseudohermaphroditism. Due to the absence or inactivity of Mullerian Inhibiting Substance (MIS), no regression is observed of the Mullerian ducts in a genotypical and phenotypical male individual. This leads to the development of fallopian tubes, uterus and proximal vagina. The testes often lie intra-abdominally and are exposed to malignant degeneration. A case is described in which the diagnosis of PMDS was made by laparotomy for an acute abdomen, caused by torsion of a seminoma.
- Published
- 1999