78 results on '"Priola, Suzette A."'
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2. The PINK1/Parkin pathway of mitophagy exerts a protective effect during prion disease
3. Efficacy of Wex-cide 128 disinfectant against multiple prion strains
4. Full-length prion protein incorporated into prion aggregates is a marker for prion strain specific destabilization of aggregate structure following cellular uptake
5. Cell biology of prion infection
6. Cell Biology Approaches to Studying Prion Diseases
7. Lack of the immune adaptor molecule SARM1 accelerates disease in prion infected mice and is associated with increased mitochondrial respiration and decreased expression of NRF2
8. Cell biology of prion strains in vivo and in vitro
9. The Size and Stability of Infectious Prion Aggregates Fluctuate Dynamically during Cellular Uptake and Disaggregation
10. β-Barrel proteins tether the outer membrane in many Gram-negative bacteria
11. Species Barriers in Prion Disease
12. Transmission characteristics of heterozygous cases of Creutzfeldt-Jakob disease with variable abnormal prion protein allotypes
13. Transgenic Mice with Neuron-Specific Expression of a Hamster Prion Protein Minigene Are Susceptible to Hamster Scrapie Agent
14. The Formation of Scrapie-Associated Prion Protein In Vitro
15. Altered distribution, aggregation, and protease resistance of cellular prion protein following intracranial inoculation
16. Processing of high-titer prions for mass spectrometry inactivates prion infectivity
17. Mitochondrial Respiration Is Impaired during Late-Stage Hamster Prion Infection
18. Prion strains depend on different endocytic routes for productive infection
19. Self-propagating, protease-resistant, recombinant prion protein conformers with or without in vivo pathogenicity
20. Cellular prion protein is present in mitochondria of healthy mice
21. PrP Knockout Cells Expressing Transmembrane PrP Resist Prion Infection
22. Relative Abundance of apoE and Aβ1–42 Associated with Abnormal Prion Protein Differs between Creutzfeldt-Jakob Disease Subtypes
23. Correction: The Distribution of Prion Protein Allotypes Differs Between Sporadic and Iatrogenic Creutzfeldt-Jakob Disease Patients
24. The Distribution of Prion Protein Allotypes Differs Between Sporadic and Iatrogenic Creutzfeldt-Jakob Disease Patients
25. Treatment of Prion Disease with Heterologous Prion Proteins
26. Proteomics applications in prion biology and structure
27. Uptake and Degradation of Protease-Sensitive and -Resistant Forms of Abnormal Human Prion Protein Aggregates by Human Astrocytes
28. Methods for Studying Prion Protein (PrP) Metabolism and the Formation of Protease-Resistant PrP in Cell Culture and Cell-Free Systems
29. Proteomics Analysis of Amyloid and Nonamyloid Prion Disease Phenotypes Reveals Both Common and Divergent Mechanisms of Neuropathogenesis
30. A Specific Population of Abnormal Prion Protein Aggregates Is Preferentially Taken Up by Cells and Disaggregated in a Strain-Dependent Manner
31. Lack of Prion Infectivity in Fixed Heart Tissue from Patients with Creutzfeldt-Jakob Disease or Amyloid Heart Disease
32. Recombinant Prion Protein Refolded with Lipid and RNA Has the Biochemical Hallmarks of a Prion but Lacks In Vivo Infectivity
33. Correction: Co-Infection with the Friend Retrovirus and Mouse Scrapie Does Not Alter Prion Disease Pathogenesis in Susceptible Mice
34. Rabbits are not resistant to prion infection
35. Identification and removal of proteins that co-purify with infectious prion protein improves the analysis of its secondary structure
36. Disinfection and Sterilization of Prion-Contaminated Medical Instruments
37. Comparative profiling of highly enriched 22L and Chandler mouse scrapie prion protein preparations
38. Comparative profiling of highly enriched 22L and Chandler mouse scrapie prion protein preparations
39. Susceptibilities of Nonhuman Primates to Chronic Wasting Disease
40. The role of the prion protein membrane anchor in prion infection
41. Cells Expressing Anchorless Prion Protein Are Resistant to Scrapie Infection
42. Prion protein misfolding and disease
43. How Animal Prions Cause Disease in Humans
44. Acute cellular uptake of abnormal prion protein is cell type and scrapie-strain independent
45. Simplified ultrasensitive prion detection by recombinant PrP conversion with shaking
46. Cyclic Tetrapyrrole Sulfonation, Metals, and Oligomerization in Antiprion Activity
47. Nonpsychoactive Cannabidiol Prevents Prion Accumulation and Protects Neurons against Prion Toxicity
48. Ultrasensitive detection of scrapie prion protein using seeded conversion of recombinant prion protein
49. Amyloid Formation via Supramolecular Peptide Assemblies
50. Molecular aspects of disease pathogenesis in the transmissible spongiform encephalopathies
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