15 results on '"Roberta Buense Bedrikow"'
Search Results
2. Consensus on the treatment of vitiligo – Brazilian Society of Dermatology☆☆☆
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Gerson Dellatorre, Daniela Alves Pereira Antelo, Roberta Buense Bedrikow, Tania Ferreira Cestari, Ivonise Follador, Daniel Gontijo Ramos, and Caio Cesar Silva de Castro
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medicine.medical_specialty ,Tratamento ,Consensus ,Vitiligo ,Disease ,Dermatology ,030207 dermatology & venereal diseases ,03 medical and health sciences ,Special Article ,0302 clinical medicine ,Quality of life ,Narrowband UVB phototherapy ,Medicine ,Combined Modality Therapy ,Humans ,Disseminated disease ,Treatment outcome ,Surgical treatment ,skin and connective tissue diseases ,Modalities ,integumentary system ,business.industry ,Clinical protocols ,Combined modality therapy ,medicine.disease ,Treatment Outcome ,Consenso ,RL1-803 ,030220 oncology & carcinogenesis ,Protocolos clínicos ,Quality of Life ,Ultraviolet Therapy ,business ,Brazil - Abstract
Background Vitiligo is a muco-cutaneous, autoimmune, localized, or disseminated disease, which manifests through hypochromic or achromic macules, with loss in quality of life. The prevalence of vitiligo in Brazil was determined to be 0.54%. There is no on-label medication for its treatment. To date, no Brazilian consensus on the treatment of vitiligo had been written. Objectives The objective of this group of Brazilian dermatologists with experience in the treatment of this disease was to reach a consensus on the clinical and surgical treatment of vitiligo, based on articles with the best scientific evidence. Methods Seven dermatologists were invited, and each was assigned two treatment modalities to review. Each treatment (topical, systemic, and phototherapy) was reviewed by three experts. Two experts reviewed the surgical treatment. Subsequently, the coordinator compiled the different versions and drafted a text about each type of treatment. The new version was returned to all experts, who expressed their opinions and made suggestions for clarity. The final text was written by the coordinator and sent to all participants to prepare the final consensus. Results/Conclusion The experts defined the following as standard treatments of vitiligo: the use of topical corticosteroids and calcineurin inhibitors for localized and unstable cases; corticosteroid minipulse in progressive generalized vitiligo; narrowband UVB phototherapy for extensive forms of the disease. Surgical modalities should be indicated for segmental and stable generalized vitiligo. Topical and systemic anti-JAK drugs are being tested, with promising results.
- Published
- 2020
3. EAACI/GA2LEN/EDF/WAO-Leitlinie für die Definition, Klassifikation, Diagnose und das Management der Urtikaria — konsentierte, deutschsprachige Übersetzung
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Mario Sánchez-Borges, Margarida Gonçalo, Elias Toubi, Ricardo Niklas Werner, Gordon Sussman, I V Danilycheva, Ana Giménez-Arnau, Corinna Dressler, Stefanie Rosumeck, Bettina Wedi, Clive Grattan, Christian Vestergaard, Franziska Ruëff, Zuotao Zhao, Karin Hartmann, Kanokvalai Kulthanan, Alexander Nast, Eustachio Nettis, Jacques Hébert, Imke Reese, Torsten Zuberbier, P. Mathelier-Fusade, Petra Staubach, Michihiro Hide, Hanneke Oude-Elberink, Thilo Jakob, Zenon Brzoza, M. Magerl, Thomas Werfel, Luis Felipe Ensina, Raisa Meshkova, Hans F. Merk, Markus Ollert, Kiran Godse, Jonathan A. Bernstein, Tabi A. Leslie, Amir Hamzah Abdul Latiff, Timothy J. Craig, Martin Metz, Peter Schmid-Grendelmeier, Hagen Ott, Sarbjit S. Saini, Roberta Buense Bedrikow, Constance H. Katelaris, Emek Kocatürk, Eckard Hamelmann, Riccardo Asero, Jürgen Grabbe, Knut Brockow, Diane Baker, Barbara Ballmer-Weber, Désirée Larenas-Linnemann, Allen P. Kaplan, Randolf Brehler, Werner Aberer, Alexander Kapp, Joachim W. Fluhr, Carsten Bindslev-Jensen, Martin K. Church, Marcus Maurer, Giorgio Walter Canonica, and Gino A. Vena
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Gynecology ,030207 dermatology & venereal diseases ,03 medical and health sciences ,medicine.medical_specialty ,0302 clinical medicine ,030228 respiratory system ,business.industry ,Immunology and Allergy ,Medicine ,business - Abstract
Diese evidenz- und konsensbasierte Leitlinie wurde entsprechend den Methoden der Cochrane und der Grading of Recommendations Assessment, Development and Evaluation (GRADE)-Arbeitsgruppen entwickelt. Die Leitlinien-Konferenz fand am 1. Dezember 2016 statt. Sie ist eine gemeinsame Initiative der European Academy of Allergology and Clinical Immunology (EAACI), dem von der EU gegrundeten Global Allergy and Asthma European Network (GA2LEN), dem European Dermatology Forum (EDF) und der World Allergy Organization (WAO) mit 48 teilnehmenden Delegierten aus 42 nationalen und internationalen Gesellschaften. Die Leitlinie ist von der European Union of Medical Specialists (UEMS) akzeptiert worden. Urtikaria ist eine haufige, mastzellabhangige Erkrankung, die mit Quaddeln, Angioodemen oder beidem einhergeht. Die Lebenszeitpravalenz der akuten Urtikaria liegt bei circa 20 %. Chronische spontane Urtikaria (CSU) und andere chronische Formen der Urtikaria sind belastend, beeintrachtigen die Lebensqualitat und haben einen negativen Einfluss auf die Leistungsfahigkeit in Beruf und Schule. Diese Leitlinie umfasst die Definition und Klassifikation der Urtikaria unter Berucksichtigung der jungsten Fortschritte in der Identifikation von Ursachen, Auslosefaktoren und Pathomechanismen. Daruber hinaus skizziert sie evidenzbasierte, diagnostische und therapeutische Ansatze fur die verschiedenen Subtypen der Urtikaria.
- Published
- 2018
4. Consensus on the diagnostic and therapeutic management of chronic spontaneous urticaria in adults - Brazilian Society of Dermatology
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Andrea Machado Coelho Ramos, Celina Wakisaka Maruta, Luis Eduardo Agner Machado Martins, Bernardo Gontijo, Maria Cecília Rivitti-Machado, Alice de Oliveira de Avelar Alchorne, Patricia Karla de Souza, Mario Cezar Pires, Roberta Buense Bedrikow, Josemir Belo dos Santos, Raquel Leão Orfali, Maria Regina Cavariani Silvares, Renan Rangel Bonamigo, Zilda Najjar Prado de Oliveira, Roberta Fachini Jardim Criado, Paulo Ricardo Criado, Universidade de São Paulo (USP), Fac Med ABC, Universidade Federal de Pernambuco (UFPE), Univ Nove Julho, Universidade Federal de Minas Gerais (UFMG), Fac Evangel Curitiba, Universidade Estadual Paulista (Unesp), Hosp Padre Bento Guarulhos, Hosp Serv Publ Estadual Sao Paulo, Universidade Federal de São Paulo (UNIFESP), Univ Fed Rio Grande do Sul, Ambulatorio Dermatol Sanitaria, Santa Casa Porto Alegre, Santa Casa Misericordia Sao Paulo, and Santa Casa Misericardia Sao Paulo
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Adult ,medicine.medical_specialty ,Histamine H1 Antagonists, Non-Sedating ,Consensus ,Urticaria ,Antagonistas dos receptores histamínicos ,Population ,MEDLINE ,Cyclosporins ,Omalizumab ,Dermatology ,Urticaria/etiology ,Severity of Illness Index ,Histamine antagonists ,030207 dermatology & venereal diseases ,03 medical and health sciences ,0302 clinical medicine ,Severity of illness ,Anti-Allergic Agents ,medicine ,Humans ,Urticarial vasculitis ,Intensive care medicine ,education ,Societies, Medical ,Urticaria/therapy ,education.field_of_study ,business.industry ,Public health ,General Medicine ,Guideline ,medicine.disease ,Work-up ,Methotrexate ,030220 oncology & carcinogenesis ,RL1-803 ,Chronic Disease ,Cyclosporine ,business ,Dapsone ,Brazil ,Immunosuppressive Agents ,medicine.drug - Abstract
Made available in DSpace on 2019-10-04T12:38:20Z (GMT). No. of bitstreams: 0 Previous issue date: 2019-03-01. Added 1 bitstream(s) on 2019-10-09T18:34:12Z : No. of bitstreams: 1 S0365-05962019000700056.pdf: 486399 bytes, checksum: a2e0a3f4581e4f634c104b420135972a (MD5) Coordenação de Aperfeiçoamento de Pessoal de Nível Superior (CAPES) BACKGROUND: Urticarias are frequent diseases, with 15% to 20% of the population presenting at least one acute episode in their lifetime. Urticaria are classified in acute ( 6 weeks). They may be induced or spontaneous. OBJECTIVES: To verify the diagnostic and therapeutic recommendations in chronic spontaneous urticaria (CSU), according to the experience of Brazilian experts, regarding the available guidelines (international and US). Methods: A questionnaire was sent to Brazilian experts, with questions concerning diagnostic and therapeutic recommendations for CSU in adults. RESULTS: Sixteen Brazilian experts answered the questionnaire related to diagnosis and therapy of CSU in adults and data were analyzed. Final text was written, considering the available guidelines (International and US), adapted to the medical practices in Brazil. Diagnostic work up in CSU is rarely necessary. Biopsy of skin lesion and histopathology may be indicated to rule out other diseases, such as, urticarial vasculitis. Other laboratory tests, such as complete blood count, CRP, ESR and thyroid screening. Treatment of CSU includes second-generation anti-histamines (sgAH) at licensed doses, sgAH two, three to fourfold doses (non-licensed) and omalizumab. Other drugs, such as, cyclosporine, immunomodulatory drugs and immunosuppressants may be indicated (non-licensed and with limited scientific evidence). CONCLUSIONS: Most of the Brazilian experts in this study partially agreed with the diagnostic and therapeutic recommendations of the International and US guidelines. They agreed with the use of sgAH at licensed doses. Increase in the dose to fourfold of sgAH may be suggested with restrictions, due to its non-licensed dose. Sedating anti-histamines, as suggested by the US guideline, are indicated by some of the Brazilian experts, due to its availability. Adaptations are mandatory in the treatment of CSU, due to scarce or lack of other therapeutic resources in the public health system in Brazil, such as omalizumab or cyclosporine. Univ Sao Paulo, Dermatol, Fac Med, Sao Paulo, SP, Brazil Fac Med ABC, Postgrad Program, Sao Paulo, SP, Brazil Univ Sao Paulo, Dept Dermatol, Fac Med, Sao Paulo, SP, Brazil Univ Fed Pernambuco, Recife, PE, Brazil Univ Nove Julho, Dermatol, Sao Paulo, SP, Brazil Univ Fed Minas Gerais, Dermatol Serv, Hosp Clin, Belo Horizonte, MG, Brazil Univ Fed Minas Gerais, Dermatol, Fac Med, Belo Horizonte, MG, Brazil Univ Fed Pernambuco, Dept Dermatol, Ctr Ciencias Med, Fac Med, Recife, PE, Brazil Fac Evangel Curitiba, Dermatol Serv, Curitiba, Parana, Brazil Univ Sao Paulo, Div Dermatol, Hosp Clin, Fac Meclicina, Sao Paulo, SP, Brazil Univ Estadual Paulista, Dept Dermatol & Radiotherapy, Botucatu, SP, Brazil Hosp Padre Bento Guarulhos, Training & Improvement Management, Sao Paulo, SP, Brazil Hosp Serv Publ Estadual Sao Paulo, Dermatol Serv, Sao Paulo, SP, Brazil Univ Fed Sao Paulo, Urticaria Outpatient Clin, Dept Dermatol, Sao Paulo, SP, Brazil Univ Fed Rio Grande do Sul, Dermatol Serv, Hosp Clin Porto Alegre, Fac Med, Porto Alegre, RS, Brazil Ambulatorio Dermatol Sanitaria, Porto Alegre, RS, Brazil Santa Casa Porto Alegre, Dermatol Serv, Porto Alegre, RS, Brazil Santa Casa Misericordia Sao Paulo, Dermatol Clin, Sao Paulo, SP, Brazil Santa Casa Misericardia Sao Paulo, Dermatol, Fac Ciencias Med, Sao Paulo, SP, Brazil Fac Med ABC, Sao Paulo, SP, Brazil Univ Estadual Paulista, Dept Dermatol & Radiotherapy, Botucatu, SP, Brazil CAPES: 001
- Published
- 2019
5. Guia prático da Associação Brasileira de Alergia e Imunologia para o diagnóstico e tratamento das urticárias baseado em diretrizes internacionais
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Joachim W. Fluhr, Torsten Zuberbier, Roberta Buense Bedrikow, Rosana Câmara Agondi, Solange Oliveira Rodrigues Valle, Luis Felipe Ensina, Regis A. Campos, Paulo Ricardo Criado, and Dirceu Solé
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- 2019
6. Lâmpada de Wood na dermatologia: aplicações na prática diária
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John Verrinder Veasey, Bárbara Arruda Fraletti Miguel, and Roberta Buense Bedrikow
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vitiligo ,melanose ,corynebacterium ,lcsh:Dermatology ,eritrasma ,tinha do couro cabeludo ,lcsh:RL1-803 ,malassézia ,porfirias ,fluorescência ,diagnóstico ,propionibacterium acnes - Abstract
A prática clínica do dermatologista baseia-se na análise das lesões cutâneas. Essa análise é feita essencialmente pela observação clínica, e atualmente complementada com exames como a dermatoscopia e a microscopia confocal. Apesar de seu baixo custo, a lâmpada de Wood tem sido cada vez menos utilizada como método diagnóstico auxiliar. Apresentamos diversos casos de utilização da lâmpada de Wood sendo de grande auxílio ao dermatologista. Esperamos assim incentivar o uso desse aparelho na prática diária.
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- 2017
7. Wood’s lamp in dermatology: applications in the daily practice
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Barbara Arruda Fraletti Miguel, Roberta Buense Bedrikow, and John Verrinder Veasey
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Surgery ,Dermatology - Published
- 2017
8. Esclerodermia cutânea: avaliação da resposta terapêutica à fototerapia
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Roberta Buense Bedrikow, Ida Alzira Gomes Duarte, Artur Antonio Duarte, and Jose Antonio Sanches Junior
- Abstract
INTRODUÇÃO: A esclerodermia é uma doença auto-imune, de evolução crônica, caracterizada pela esclerose progressiva do tecido conjuntivo e alterações da microcirculação. A etiologia da doença ainda não está esclarecida. Em sua patogênese ocorre dano no endotélio vascular, com ativação inflamatória e imunológica, levando ao aumento da síntese do colágeno e outras proteínas da matriz extracelular. A esclerodermia cutânea é uma doença autolimitada e as formas superficiais evoluem com resolução em meses ou anos, deixando pouca ou nenhuma seqüela. Entretanto, em dez por cento dos casos ocorrem lesões atróficas, deformantes, que retardam ou dificultam o desenvolvimento normal. Relatos da literatura apontam a fototerapia como uma modalidade terapêutica com resposta favorável nas formas cutâneas da esclerodermia. A fototerapia, através do seu efeito imunossupressor, inibe a produção do colágeno além de induzir aumento da síntese de colagenase. Este trabalho teve como objetivo avaliar o tratamento da esclerodermia cutânea com fototerapia. Utilizou-se o exame clínico e a ultra-sonografia da pele como metodologia para demonstrar os resultados obtidos com o tratamento proposto. MÉTODOS: Durante o período de janeiro a dezembro de 2007, foram selecionados 11 pacientes com diagnóstico de esclerodermia cutânea, para o tratamento com fototerapia no Setor de Alergia e Fototerapia da Clínica de Dermatologia da Santa Casa de São Paulo. Os pacientes foram classificados de acordo com o tipo de esclerodermia cutânea e o estágio evolutivo das lesões: inflamatórias ou de estado. Os tipos de fototerapia escolhidos para esse estudo foram PUVA sistêmico, PUVA tópico e UVB banda estreita. As lesões foram avaliadas pela palpação clínica em busca de resistência ao pinçamento da pele, e submetidas ao exame de ultra-som de alta freqüência, com a finalidade de mensurar a espessura da derme, antes do tratamento e ao final da 12ª semana de fototerapia. RESULTADOS: Foi observado o início da melhora clínica das lesões com média de 10 sessões de fototerapia. A palpação clínica mostrou amolecimento em todas as lesões estudadas, tanto em lesões inflamatórias como nas lesões de estado, com redução nos escores quando comparado pré e pós-tratamento. No exame de ultra-som, a maioria das lesões avaliadas mostrou diminuição da espessura da derme e apenas cinco mantiveram sua medida. Não se observou diferença na resposta ao tratamento de acordo com o tipo de fototerapia instituída. CONCLUSÕES: O tratamento proposto foi efetivo em todas as lesões, independentemente do tipo de fototerapia realizada. A melhora foi observada em todas as lesões tratadas, e comprovada pela avaliação clínica e exame de ultra-som da pele INTRODUCTION: Scleroderma is a chronic autoimmune disease characterized by progressive connective tissue sclerosis and microcirculatory changes. Its etiology is still unknown. Its pathogenesis shows endothelial cell damage, inflammation and immunologic activation that stimulate collagen and other extra cellular matrix protein production. Localized scleroderma is a limited disease and its superficial forms may be resolved in months or years, and leave little or no sequel. However, in ten percent of the cases atrophic and deforming lesions may be observed that delay or hinder normal development. Literature reports indicate phototherapy as a limited scleroderma therapeutic modality with favorable response. Through its immunosuppressant effect, phototherapy inhibits collagen production and induces increased collagenase synthesis. This study had the purpose of evaluating the phototherapy treatment for localized scleroderma. The clinical evaluation and the skin ultrasound were used to demonstrate the results thus obtained. METHODS: From January to December 2007, eleven patients with localized scleroderma were selected for phototherapy treatment in the Allergy and Phototherapy Division, Dermatology Clinic, Santa Casa of São Paulo Hospital. They were classified according to the type of localized scleroderma and lesion evolution: inflammatory or stadial. The lesions were treated with systemic PUVA, topic PUVA or UVB narrow band. The skin lesions were assessed by clinical palpation and high-frequency ultrasound to measure dermis thickness at baseline and at the end of 12 weeks of phototherapy. RESULTS: Some clinical improvement was observed after an average of 10 phototherapeutic sessions. All skin lesions, either inflammatory or stadial, were softer at clinical palpation with scores reduction upon pre and post treatment comparison. The ultrasound showed that most of the assessed lesions presented a decrease in dermis thickness, and only five maintained their previous measure. Treatment response was similar regardless of the phototherapeutic treatment employed. CONCLUSIONS: The treatment that was proposed was effective for all the lesions, regardless of the phototherapeutic modality employed. The improvement was observed in all skin lesions and evidenced by clinical evaluation and skin ultrasound
- Published
- 2015
9. Qual é o tipo de fototerapia mais comumente indicada no tratamento da psoríase?: UVB banda estreita e PUVA: comportamento da prescrição
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José Antonio Jabur da Cunha, Rosana Lazzarini, Ida Duarte, and Roberta Buense Bedrikow
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medicine.medical_specialty ,Skin type ,business.industry ,Fototerapia ,Narrow band uvb ,Dermatology ,Terapia PUVA ,Psoríase ,medicine.disease ,Raios Ultravioleta ,chemistry.chemical_compound ,Liver disease ,Refractory ,chemistry ,Psoriasis ,medicine ,Severe psoriasis ,Medical prescription ,business ,Psoralen - Abstract
BACKGROUND Moderate and severe forms of psoriasis require phototherapy and / or systemic medications. Both UVA and UVB can be used to treat cases of moderate and severe psoriasis, and the effectiveness of both has been proven. OBJECTIVE to access the prescription behavior relating to two types of phototherapy for treating psoriasis refractory to topical treatment: narrowband UVB (NB-UVB) or psoralen plus UVA phototherapy (PUVA). METHODS Between January 2006 and December 2007, patients referred to two phototherapy services were included in this study. Data on the cases and on the type of prescription were collected retrospectively. RESULTS Among the 67 studied patients, 51 (76%) were treated with narrowband UVB. The reasons for the indication were the presence of the guttate type of psoriasis (22%), the presence of thin plaques (15%), the use of drugs that affected photosensitivity (15%), age less than 20 years (9%), skin type I (9%), and liver disease (6%). The remaining 16 (24%) were treated with PUVA. The main indication for this therapy was the severity of the disease (15%), followed by the presence of skin type IV (9%). CONCLUSIONS Prescriptions of narrowband UVB exceeded those of PUVA because of fewer contraindications and fewer possible side effects, and because it was a more practical option.
- Published
- 2009
10. Qual é o tipo de fototerapia mais comumente indicada no tratamento da psoríase?: UVB banda estreita e PUVA: comportamento da prescrição What is the most common phototherapy prescription for psoriasis: NB-UVB or PUVA? Prescription behavior
- Author
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Ida Duarte, José Antonio Jabur da Cunha, Roberta Buense Bedrikow, and Rosana Lazzarini
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Raios Ultravioleta ,PUVA therapy ,Ultraviolet rays ,Fototerapia ,lcsh:Dermatology ,Psoriasis ,Terapia PUVA ,Phototherapy ,lcsh:RL1-803 ,Psoríase - Abstract
FUNDAMENTOS: Formas moderada e grave de psoríase requerem fototerapia e/ou medicações sistêmicas. Tanto UVB banda estreita quanto fototerapia UVA com psoralênicos (PUVA) podem ser utilizadas no tratamento dessas formas de psoríase, sendo comprovada a efetividade de ambas as terapias. OBJETIVOS: Avaliar as indicações de dois tipos de fototerapia no tratamento da psoríase refratária à terapia tópica: UVB banda estreita e PUVA. MÉTODOS: Entre janeiro de 2006 e dezembro de 2007, os pacientes encaminhados a dois serviços de fototerapia foram incluídos neste estudo. Dados sobre os casos e tipos de prescrição foram coletados de maneira retrospectiva. RESULTADOS: Dentre os 67 pacientes estudados, 51 (76%) foram tratados com UVB banda estreita. As razões para sua indicação foram presença de psoríase em gotas (22%), presença de finas placas (15%), uso de drogas fotossensibilizantes (15%), idade abaixo de 20 anos (9%), fototipo I (9%) e doença hepática (6%). Os 16 (24%) restantes foram tratados com PUVA. A principal indicação dessa terapia foi gravidade da doença (15%), seguida de fototipo IV (9%). CONCLUSÕES: As prescrições de UVB banda estreita excederam as de PUVA devido ao menor número de contraindicações, menor possibilidade de efeitos colaterais, e ainda por ser uma opção mais prática.BACKGROUND: Moderate and severe forms of psoriasis require phototherapy and / or systemic medications. Both UVA and UVB can be used to treat cases of moderate and severe psoriasis, and the effectiveness of both has been proven. OBJECTIVE: to access the prescription behavior relating to two types of phototherapy for treating psoriasis refractory to topical treatment: narrowband UVB (NB-UVB) or psoralen plus UVA phototherapy (PUVA). METHODS: Between January 2006 and December 2007, patients referred to two phototherapy services were included in this study. Data on the cases and on the type of prescription were collected retrospectively. RESULTS: Among the 67 studied patients, 51 (76%) were treated with narrowband UVB. The reasons for the indication were the presence of the guttate type of psoriasis (22%), the presence of thin plaques (15%), the use of drugs that affected photosensitivity (15%), age less than 20 years (9%), skin type I (9%), and liver disease (6%). The remaining 16 (24%) were treated with PUVA. The main indication for this therapy was the severity of the disease (15%), followed by the presence of skin type IV (9%). CONCLUSIONS: Prescriptions of narrowband UVB exceeded those of PUVA because of fewer contraindications and fewer possible side effects, and because it was a more practical option.
- Published
- 2009
11. Fototerapia na doença enxerto contra hospedeiro Phototherapy in the graft versus host disease
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Ida Duarte, Paula Voltarelli, Rosana Lazzarini, and Roberta Buense Bedrikow
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Raios ultravioleta ,PUVA therapy ,Ultraviolet rays ,Doença enxerto-hospedeiro ,Fototerapia ,lcsh:Dermatology ,Terapia Puva ,Phototherapy ,lcsh:RL1-803 ,Graft versus host disease - Abstract
FUNDAMENTOS: A doença enxerto contra hospedeiro é um dos obstáculos ao sucesso do transplante de medula óssea, e o envolvimento cutâneo é freqüente. A fototerapia é utilizada devido à intensa atividade imunomoduladora local, sendo opção terapêutica adjuvante para as lesões cutâneas resistentes à terapia convencional. OBJETIVO: Realizar análise descritiva do tratamento da doença enxerto contra hospedeiro com fototerapia (Puva ou UVB de faixa estreita). MÉTODOS: Foram atendidos nove pacientes com manifestação cutânea da doença enxerto contra hospedeiro aguda ou crônica. Seis foram tratados com Puva, terapia de primeira escolha, e três com UVB de faixa estreita. As sessões foram realizadas três vezes por semana, e a resposta terapêutica avaliada após 12 sessões. RESULTADOS: Todos os pacientes com doença enxerto contra hospedeiro aguda mostraram melhora, com desaparecimento do eritema e do edema. Naqueles com doença crônica, observaram-se involução das lesões liquenóides e melhora da mobilidade daqueles com a forma esclerodermiforme. Dois pacientes apresentaram doença de evolução grave e foram a óbito. CONCLUSÃO: A fototerapia mostrou-se efetiva no tratamento das manifestações cutâneas da doença enxerto contra hospedeiro aguda e crônica. A Puva permite o controle da doença, podendo a UVB de faixa estreita ser opção para pacientes impossibilitados de usar medicação sistêmica.BACKGROUND: Graft versus host disease is one of the obstacles to successful bone marrow transplantation. It often affects the skin. Phototherapy has been used because of its strong local immunomodulatory activity and it is an option for adjuvant therapy for skin lesions of graft versus host disease resistant to conventional therapy. OBJECTIVE: To make a descriptive analysis of treating graft versus host disease with phototherapy (PUVA or narrowband UVB). Methods - Nine patients with cutaneous manifestation of acute or chronic graft versus host disease were studied. The first choice therapy was PUVA, applied in six patients, and three were treated with narrowband UVB. The sessions were held three times a week and therapeutic response was evaluated after 12 sessions. RESULTS: All patients with acute graft versus host disease showed improvement, with the disappearance of erythema and edema. In those with chronic graft versus host disease, there was good response to therapy with regression of lichenoid lesions and better mobility of patients with the sclerodermoid form. Two patients had severe progression and died. CONCLUSION: Phototherapy showed to be effective in treating skin manifestations of acute and chronic graft versus host disease. PUVA allows control of the disease. The narrowband UVB is an option for patients who cannot take systemic medications.
- Published
- 2008
12. Você conhece esta síndrome? Do you know this syndrome?
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Roberta Buense Bedrikow, Débora Cadore de Farias, Marcus Maia, and Helena Müller
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Osteoarthropathy, primary hypertrophic ,lcsh:Dermatology ,Dermatoses faciais ,Osteoartropatia hipertrófica primária ,Hyperostosis ,lcsh:RL1-803 ,Facial dermatoses ,Hiperostose - Abstract
Paquidermoperiostose é genodermatose autossômica dominante rara, que afeta pele e ossos, porém sua prevalência e incidência permanecem desconhecidas. Ocorre predominantemente em homens, que também mostram fenótipo mais grave da doença. Descrevese o caso de paciente do sexo masculino, de 60 anos.Pachydermoperiostosis is a rare autosomal dominant genodermatosis characterized by bone and cutaneous involvement, even though its prevalence and incidence are ignored. It occurs predominantly in men, which present a more serious clinical presentation. We report a case of a 60-year-old man with this disease.
- Published
- 2007
13. What is the most common phototherapy prescription for psoriasis: NB-UVB or PUVA? Prescription behavior
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Ida, Duarte, José Antonio Jabur da, Cunha, Roberta Buense, Bedrikow, and Rosana, Lazzarini
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Adult ,Aged, 80 and over ,Male ,Adolescent ,Middle Aged ,Phototherapy ,Severity of Illness Index ,Young Adult ,Prescriptions ,Humans ,Psoriasis ,Female ,Ultraviolet Therapy ,Child ,PUVA Therapy ,Aged ,Retrospective Studies - Abstract
Moderate and severe forms of psoriasis require phototherapy and / or systemic medications. Both UVA and UVB can be used to treat cases of moderate and severe psoriasis, and the effectiveness of both has been proven.to access the prescription behavior relating to two types of phototherapy for treating psoriasis refractory to topical treatment: narrowband UVB (NB-UVB) or psoralen plus UVA phototherapy (PUVA).Between January 2006 and December 2007, patients referred to two phototherapy services were included in this study. Data on the cases and on the type of prescription were collected retrospectively.Among the 67 studied patients, 51 (76%) were treated with narrowband UVB. The reasons for the indication were the presence of the guttate type of psoriasis (22%), the presence of thin plaques (15%), the use of drugs that affected photosensitivity (15%), age less than 20 years (9%), skin type I (9%), and liver disease (6%). The remaining 16 (24%) were treated with PUVA. The main indication for this therapy was the severity of the disease (15%), followed by the presence of skin type IV (9%).Prescriptions of narrowband UVB exceeded those of PUVA because of fewer contraindications and fewer possible side effects, and because it was a more practical option.
- Published
- 2009
14. Fototerapia na doença enxerto contra hospedeiro
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Rosana Lazzarini, Roberta Buense Bedrikow, Paula Voltarelli, and Ida Duarte
- Subjects
Raios ultravioleta ,Doença enxerto-hospedeiro ,Fototerapia ,Dermatology ,Terapia Puva - Abstract
FUNDAMENTOS: A doença enxerto contra hospedeiro é um dos obstáculos ao sucesso do transplante de medula óssea, e o envolvimento cutâneo é freqüente. A fototerapia é utilizada devido à intensa atividade imunomoduladora local, sendo opção terapêutica adjuvante para as lesões cutâneas resistentes à terapia convencional. OBJETIVO: Realizar análise descritiva do tratamento da doença enxerto contra hospedeiro com fototerapia (Puva ou UVB de faixa estreita). MÉTODOS: Foram atendidos nove pacientes com manifestação cutânea da doença enxerto contra hospedeiro aguda ou crônica. Seis foram tratados com Puva, terapia de primeira escolha, e três com UVB de faixa estreita. As sessões foram realizadas três vezes por semana, e a resposta terapêutica avaliada após 12 sessões. RESULTADOS: Todos os pacientes com doença enxerto contra hospedeiro aguda mostraram melhora, com desaparecimento do eritema e do edema. Naqueles com doença crônica, observaram-se involução das lesões liquenóides e melhora da mobilidade daqueles com a forma esclerodermiforme. Dois pacientes apresentaram doença de evolução grave e foram a óbito. CONCLUSÃO: A fototerapia mostrou-se efetiva no tratamento das manifestações cutâneas da doença enxerto contra hospedeiro aguda e crônica. A Puva permite o controle da doença, podendo a UVB de faixa estreita ser opção para pacientes impossibilitados de usar medicação sistêmica.
- Published
- 2008
15. Você conhece esta síndrome?
- Author
-
Roberta Buense Bedrikow, Débora Cadore de Farias, Marcus Maia, and Helena Müller
- Subjects
Dermatology ,Dermatoses faciais ,Osteoartropatia hipertrófica primária ,Hiperostose - Abstract
Paquidermoperiostose é genodermatose autossômica dominante rara, que afeta pele e ossos, porém sua prevalência e incidência permanecem desconhecidas. Ocorre predominantemente em homens, que também mostram fenótipo mais grave da doença. Descrevese o caso de paciente do sexo masculino, de 60 anos.
- Published
- 2007
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