32 results on '"Futerman, Anthony H"'
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2. Altered lysosome distribution is an early neuropathological event in neurological forms of Gaucher disease
3. Innate immune responses in the brain of sphingolipid lysosomal storage diseases
4. Sphingoid long chain bases prevent lung infection by Pseudomonas aeruginosa
5. Neuronal accumulation of glucosylceramide in a mouse model of neuronopathic Gaucher disease leads to neurodegeneration
6. Identification of N-acyl-fumonisin B1 as new cytotoxic metabolites of fumonisin mycotoxins
7. Ablation of Very Long Acyl Chain Sphingolipids Causes Hepatic Insulin Resistance in Mice Due to Altered Detergent-Resistant Membranes
8. Contribution of brain inflammation to neuronal cell death in neuronopathic forms of Gaucherʼs disease
9. Comparison of a molecular dynamics model with the X-ray structure of the N370S acid-β-glucosidase mutant that causes Gaucher disease
10. Lysosomal Storage Disorders and ParkinsonʼS Disease: Gaucher Disease and Beyond
11. Spatial and temporal correlation between neuron loss and neuroinflammation in a mouse model of neuronopathic Gaucher disease
12. Altered expression and distribution of cathepsins in neuronopathic forms of Gaucher disease and in other sphingolipidoses
13. Cellular pathogenesis in sphingolipid storage disorders: the quest for new therapeutic approaches
14. Stress-induced ER to Golgi translocation of ceramide synthase 1 is dependent on proteasomal processing
15. Characterization of gene-activated human acid-β-glucosidase: Crystal structure, glycan composition, and internalization into macrophages
16. No evidence for activation of the unfolded protein response in neuronopathic models of Gaucher disease
17. Acid β-glucosidase: insights from structural analysis and relevance to Gaucher disease therapy
18. An exposed carboxyl group on sialic acid is essential for gangliosides to inhibit calcium uptake via the sarco/endoplasmic reticulum Ca2+-ATPase: relevance to gangliosidoses
19. Preface
20. An appreciation of Dr Steven Pfeiffer, 1940–2007
21. CELL BIOLOGY: Taxi service for lipids
22. Reversion of the biochemical defects in murine embryonic Sandhoff neurons using a bicistronic lentiviral vector encoding hexosaminidase α and β
23. Defective calcium homeostasis in the cerebellum in a mouse model of Niemann–Pick A disease
24. Gaucher disease: pathological mechanisms and modern management
25. Phospholipid synthesis is decreased in neuronal tissue in a mouse model of Sandhoff disease
26. Glycosphingolipidoses: Beyond the enzymatic defect
27. The roles of ceramide and complex sphingolipids in neuronal cell function
28. The Role of Sphingolipids in Neuronal Development: Lessons from Models of Sphingolipid Storage Diseases
29. Cholesterol depletion by methyl-β-cyclodextrin blocks cholera toxin transport from endosomes to the Golgi apparatus in hippocampal neurons
30. Regulatory Roles for Sphingolipids in the Growth of Polarized Neuronsa
31. Glucosylceramide Synthesis Is Required for Basic Fibroblast Growth Factor and Laminin to Stimulate Axonal Growth
32. Rate of Retrograde Transport of Cholera Toxin from the Plasma Membrane to the Golgi Apparatus and Endoplasmic Reticulum Decreases During Neuronal Development
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