1. Complicaţiile cirozei la un pacient cu atrezie de căi biliare.
- Author
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Gălăţan, Ana-Georgeta, Grama, Alina, and Pop, Tudor Lucian
- Abstract
Cirrhosis is the frightening complication of chronic liver disease. Common causes include biliary atresia, a pathology with a poor prognosis in the absence of a prompt diagnosis and therapeutic intervention. We present the case of a patient diagnosed with biliary atresia who underwent Kasai intervention. After an initial period with disappearance of the jaundice and normal color of the stool, the patient reached the stage of decompensated cirrhosis. Among the complications suffered by the patient we mention ascites, esophageal varices, upper gastrointestinal hemorrhage, repeated infections, anemia, rickets, and hepatic osteodystrophy. For this patient, the only long-term therapeutic option remains liver transplantation. Although cases of pediatric patients with an early Kasai intervention and survival with native liver are described, the long-term evolution depends on the occurrence of possible complications and most patients eventually require liver transplantation. [ABSTRACT FROM AUTHOR]
- Published
- 2019